European Headache Federation guideline on idiopathic intracranial hypertension | The Journal of Headache and Pain | Full Text

European Headache Federation guideline on idiopathic intracranial hypertension | The Journal of Headache and Pain | Full Text

The Journal of Headache and Pain

European Headache Federation guideline on idiopathic intracranial hypertension

• Jan HoffmannEmail authorView ORCID ID profile,
• Susan P Mollan,
• Koen Paemeleire,
• Christian Lampl,
• Rigmor H Jensen and
• Alexandra J Sinclair

The Journal of Headache and PainOfficial Journal of the "European Headache Federation" and of "Lifting The Burden - The Global Campaign against Headache"201819:93

https://doi.org/10.1186/s10194-018-0919-2

©  The Author(s). 2018

• Received: 31 July 2018
• Accepted: 14 September 2018
• Published: 8 October 2018

Abstract

Background

Idiopathic Intracranial Hypertension (IIH) is characterized by an elevation of intracranial pressure (ICP no identifiable cause. The aetiology remains largely unknown, however observations made in a number of recent clinical studies are increasing the understanding of the disease and now provide the basis for evidence-based treatment strategies.

Methods

The Embase, CDSR, CENTRAL, DARE and MEDLINE databases were searched up to 1st June 2018. We analyzed randomized controlled trials and systematic reviews that investigate IIH.

Results

Diagnostic uncertainty, headache morbidity and visual loss are among the highest concerns of clinicians and patients in this disease area. Research in this field is infrequent due to the rarity of the disease and the lack of understanding of the underlying pathology.

Conclusions

This European Headache Federation consensus paper provides evidence-based recommendations and practical advice on the investigation and management of IIH.